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Stiehm’s Immune Deficiencies, 1ed

Stiehm’s Immune Deficiencies focuses on immunodeficiencies in children and adults.  This book covers the many advances in the study of immunodeficiency. Stiehm’s Immune Deficiencies includes 62 chapters covering topics such as newly described syndromes, genetic diagnosis, molecular abnormalities, newborn screening, and current therapies.

  • Provides practical guidance to practitioners dealing with the day-to-day issues of diagnosis and management of immune deficient patients
  • Covers both clinical management and scientific advances in one place
  • Includes newly described disorders in various periodic updates to maintain the breadth of the reference

Review

“…a detailed, high-quality book on the diagnosis and management of patients with immune deficiency syndromes. It addresses issues of patient care as well as current research data, and presents information on differential diagnoses and data on the use of laboratory analyses. Score: 97 – 5 Stars” —Doody’s

“…appealing to an extended audience including general internists, infectious disease specialists, rheumatologists, and all physicians dealing with transplant recipients…an excellent reference book inthe field of immunology that should be part of every library.” —Clinical Infectious Diseases

About the Author

Professor of Pediatrics, at the Children’s Hospital of Philadelphia, Philadelphia, PA, USA

B.A., M.A. (Biophysics), Johns Hopkins University, 1980. Ph.D. (Immunology & Biochemistry)

University of California at San Francisco, 1988. M.D. University of California at San Francisco, 1988.

MD, University of Wisconsin Medical School 1957

Affiliated at: Ronald Reagan UCLA Medical Center

Contents

۱ Common Presentations and Diagnostic Approaches
۲ Overview of Laboratory Studies for Evaluating Primary Immune Deficiency Disorders
۳ Genetics of Primary Immune Deficiencies
۴ Severe Combined Immunodeficiencies
۵ Combined Immune Deficiencies
۶ Well-Known Combined Immune Deficiency Syndromes
۷ DNA Repair Defects
۸ Defects in Thymic Development: DiGeorge/CHARGE/Chromosome 22qll.2 Deletion
۹ Idiopathic CD4 Lymphopenia
۱۰ Hyper IgE Syndrome (STAT3 Defect)
۱۱ Dyskeratosis Congenita
۱۲ Genetic Syndromes with Evidence of Immune Deficiency
۱۳ Agammaglobulinemia
۱۴ Hypogammaglobulinemia and Common Variable Immunodeficiency
۱۵ Class-Switch Recombination Defects
۱۶ Isotype Defects
۱۷ Specific Antibody Deficiency with Normal Immunoglobulins
۱۸ Transient Hypogammaglobulinemia of Infancy
۱۹ Centromeric Instability in ICF Syndrome
۲۰ Genetic Diseases Predisposing to HLH
۲۱ Autoimmune Lymphoproliferative Syndromes
۲۲ The X-Linked Lymphoprolferative Syndromes
۲۳ Immune Dysregulation Leading to Chronic Autoimmunity
۲۴ Classic Autoinflammatory Diseases
۲۵ Autoinflammatory Diseases Predominantly Affecting Bone and Joints
۲۶ Autoinflammatory Diseases Predominantly Affecting the Gastrointestinal Tract
۲۷ Autoinflammatory Diseases Affecting Predominantly the Skin
۲۸ Mendelian Disorders of Immunity Related to an Upregulation of TypeIInterferon
۲۹ Congenital Neutropenia
۳۰ Neutrophil Migration Defects
۳۱ Chronic Granulomatous Disease
۳۲ Macrophage Defects
۳۳ Human Immunodeficiencies Resulting From Defective NF-KB Activation
۳۴ Other TLR Pathway Defects
۳۵ Warts, Hypogammaglobulinemiar Infectionsr and Myelokathexis Syndrome
۳۶ STAT2
۳۷ Epidermodysplasia Verruciformis
۳۸ Deficiencies of the Complement System
۳۹ Natural Killer Cell Deficiency
۴۰ Mucocutaneous Candidiasis
۴۱ Immune Compromise Due to Immaturity
۴۲ Immune Compromise in the Elderly
۴۳ Immunologic Changes During Pregnancy
۴۴ Immune Compromise Due to Metabolic Disorders
۴۵ Asplenia
۴۶ Infections That Cause Secondary Immunodeficiency
۴۷ Protein-Losing Conditions
۴۸ The Impact of Malignancy on Adaptive Immunity
۴۹ Immune Compromise Associated with Biologies
۵۰ Autoantibody-Mediated Phenocopies of Primary Immunodeficiency Diseases
۵۱ Prevention and Management of Infections
۵۲ Management of Autoimmunity and Inflammation
۵۳ Considerations for Primary Immune Deficiency Disorders in South America
۵۴ Considerations for Primary Immune Deficiency Disorders in Africa and the Middle East
۵۵ Considerations for Primary Immune Deficiency Disorders in Asia
۵۶ Immunoglobulin Replacement
۵۷ Vaccination of Immune-Deficient Patients
۵۸ Hematopoietic Stem Cell Transplantation for Primary Immunodeficiency
۵۹ Gene Therapy for Primary Immune Deficiencies
۶۰ Thymus Transplantation
۶۱ Registries
۶۲ Resources for Clinicians

جهت مشاهده ویرایش ۲۰۲۰ این کتاب کلیک کنید

قیمت : 6000 تومان

لینک کوتاه : https://bookbaz.ir/?p=54237
نویسنده : E. Richard Stiehm MD
ناشر : Academic Press; 1 edition
سال انتشار : 2015
زبان کتاب : انگلیسی
نوع فایل : PDF
تعداد صفحات : 1157
(ISBN) شابک : 012405546X
قیمت کتاب درآمازون : $289.56
حجم فایل : 21 MB

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